| Abstract | UVOD: Parcijalni anomalni utok plućnih vena (PAUPV) prirođena je srčana greška u
kojoj jedna ili više plućnih vena, ali ne sve, utječu u sistemsku vensku cirkulaciju.
Liječenje PAUPV-a je gotovo isključivo kirurško, a najčešće korištene kirurške tehnike su
tehnika jednostruke zakrpe, tehnika dvostruke zakrpe te Wardenova tehnika.
----- CILJ: Prikazati karakteristike pacijenata operiranih zbog PAUPV-a u Kliničkom
bolničkom centru Zagreb od 2011. do 2019. godine.
----- ISPITANICI I METODE: U istraživanje je uključeno 35 osoba (20 muškog i 15 ženskog
spola). Demografski podaci, podaci o morfologiji greške, podaci o kliničkoj slici i
dijagnostici, te podaci o operaciji i postoperativnom razdoblju prikupljeni su s Bolničkog
informacijskog sustava.
----- REZULTATI: Ispitanici su prema uzrastu svrstani u kategoriju djece (N=18) i kategoriju
odraslih s prirođenim srčanim greškama (N=17). Dvoje pacijenata imalo je ljevostrani
PAUPV, a dvoje sindrom scimitar. Izolirani PAUPV imalo je 6,1% ispitanika, a najčešća
pridružena anomalija bio je ASD (84,8%). Simptome prilikom postavljanja dijagnoze
imalo je 62,9% ispitanika. Najčešća metoda kojom je postavljena dijagnoza bila je
ehokardiografija (52,9%). Kod 32,4% pacijenata PAUPV je korigiran tehnikom
jednostruke zakrpe, a kod 61,8% tehnikom dvostruke zakrpe. Preživljenje nakon
operacije bilo je 100%. Kod sedam je pacijenata nastala komplikacija, koja je kod dvoje
iziskivala reoperaciju, a kod troje se radilo o novonastaloj aritmiji.
----- ZAKLJUČAK: Morfologija PAUPV-a, kliničke manifestacije te rezultati kirurškog liječenja
u proučavanom uzorku odgovaraju onima iz literaturnih izvora. |
| Abstract (english) | INTRODUCTION: Partial anomalous pulmonary venous connection (PAPVC) is a
congenital heart defect in which one or more, but not all, pulmonary veins connect to
systemic venous circulation. PAPVC treatment is almost exclusively surgical, most
commonly used surgical procedures being single patch, double patch and Warden
procedure.
----- AIM: To present the characteristics of patients from University Hospital Centre Zagreb in
which PAPVC repair was done in the period from 2011 to 2019.
----- SUBJECTS AND METHODS: 35 patients (20 male and 15 female) were included in this
research. Demographical data, information about morphology of the defect, clinical
presentation and date regarding the surgery and postoperative period were obtained
using hospital information system.
----- RESULTS: The subjects were, in regard to age, assigned to a category of children
(N=18) or grown-ups with congenital heart defects (N=17). Two patients had a left-sided
PAPVC while two had scimitar syndrome. Isolated PAPVC was present in 6.1% of
subjects and most common associated heart defect was ASD (84.8%). Symptoms were
present in 62.9% upon diagnosis. Most common method used as diagnostic procedure
was echocardiography (52.9%). In 32.4% of patients, single patch procedure was used
to repair PAPVC, while double patch procedure was used in 61.8% of patients. Survival
was 100% in postoperative period. A complication of surgery occurred in seven
patients, requiring reintervention in two patients and in three being the case of newly
discovered arrhythmia.
----- CONCLUSION: PAPVC morphology, clinical presentation and surgical treatment results
in this sample are similar to those described in literature. |
