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S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV)
Journal of the European Academy of Dermatology and Venereology, 37 (2023), 6; 1118-1134. https://doi.org/10.1111/jdv.18931
Antiga, Emiliano; Bech, Rikke; Maglie, Roberto; Genovese, Giovanni; Borradori, Luca; Bockle, Barbara; Caproni, Marzia; Caux, Frédéric; Chandran, Nisha Suyien; Corrà, Alberto; D'Amore, Francesco; Daneshpazhooh, Maryam; De, Dipankar; Didona, Dario; Dmochowski, Marian; Drenovska, Kossara; Ehrchen, Jan; Feliciani, Claudio; Goebeler, Matthias; Groves, Richard; Günther, Claudia; Handa, Sanjeev; Hofmann, Silke C.; Horvath, Barbara; Ioannidis, Dimitrios; Jedlickova, Hana; Kowalewski, Cezary; Kridin, Khalaf; Joly, Pascal; Lim, Yen Loo; Marinović, Branka; Maverakis, Emanual; Meijer, Joost; Patsatsi, Aikaterini; Pincelli, Carlo; Prost, Catherine; Setterfield, Jane; Sprecher, Eli; Skiljevic, Dusan; Tasanen, Kaisa; Uzun, Soner; Van Beek, Nina; Vassileva, Snejina; Vorobyev, Artem; Vujic, Igor; Wang, Gang; Wang, Mingyue; Wozniak, Katarzyna; Yayli, Savas; Zambruno, Giovanna; Hashimoto, Takashi; Schmidt, Enno; Mascarò, José Manuel; Marzano, Angelo Valerio Više autora...

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Antiga, E., Bech, R., Maglie, R., Genovese, G., Borradori, L., Bockle, B. ... Marzano, A. V. (2023). S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV). Journal of the European Academy of Dermatology and Venereology, 37. (6), 1118-1134. doi: 10.1111/jdv.18931

Antiga, Emiliano, et al. "S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV)." Journal of the European Academy of Dermatology and Venereology, vol. 37, br. 6, 2023, str. 1118-1134. https://doi.org/10.1111/jdv.18931

Antiga, Emiliano, Rikke Bech, Roberto Maglie, Giovanni Genovese, Luca Borradori, Barbara Bockle, Marzia Caproni, et al. "S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV)." Journal of the European Academy of Dermatology and Venereology 37, br. 6 (2023): 1118-1134. https://doi.org/10.1111/jdv.18931

Antiga, E., et al. (2023) 'S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV)', Journal of the European Academy of Dermatology and Venereology, 37(6), str. 1118-1134. doi: 10.1111/jdv.18931

Antiga E, Bech R, Maglie R, Genovese G, Borradori L, Bockle B, i sur.. S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV). Journal of the European Academy of Dermatology and Venereology [Internet]. 25.03.2023. [pristupljeno 05.10.2024.];37(6):1118-1134. doi: 10.1111/jdv.18931

E. Antiga, et al., "S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV)", Journal of the European Academy of Dermatology and Venereology, vol. 37, br. 6, str. 1118-1134, Ožujak 2023. [Online]. Dostupno na: https://urn.nsk.hr/urn:nbn:hr:105:818244. [Citirano: 05.10.2024.]

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Naslov (engleski)S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV)
AutorEmiliano Antiga
AutorRikke Bech
AutorRoberto Maglie
AutorGiovanni Genovese
AutorLuca Borradori
AutorBarbara Bockle
AutorMarzia Caproni
AutorFrédéric Caux
AutorNisha Suyien Chandran
AutorAlberto Corrà
AutorFrancesco D'Amore
AutorMaryam Daneshpazhooh
AutorDipankar De
AutorDario Didona
AutorMarian Dmochowski
AutorKossara Drenovska
AutorJan Ehrchen
AutorClaudio Feliciani
AutorMatthias Goebeler
AutorRichard Groves
AutorClaudia Günther
AutorSanjeev Handa
AutorSilke C. Hofmann
AutorBarbara Horvath
AutorDimitrios Ioannidis
AutorHana Jedlickova
AutorCezary Kowalewski
AutorKhalaf Kridin
AutorPascal Joly
AutorYen Loo Lim
AutorBranka Marinović
AutorEmanual Maverakis
AutorJoost Meijer
AutorAikaterini Patsatsi
AutorCarlo Pincelli
AutorCatherine Prost
AutorJane Setterfield
AutorEli Sprecher
AutorDusan Skiljevic
AutorKaisa Tasanen
AutorSoner Uzun
AutorNina Van Beek
AutorSnejina Vassileva
AutorArtem Vorobyev
AutorIgor Vujic
AutorGang Wang
AutorMingyue Wang
AutorKatarzyna Wozniak
AutorSavas Yayli
AutorGiovanna Zambruno
AutorTakashi Hashimoto
AutorEnno Schmidt
AutorJosé Manuel Mascarò
AutorAngelo Valerio Marzano
Autorova ustanovaSveučilište u Zagrebu
Medicinski fakultet
(KATEDRA ZA DERMATOVENEROLOGIJU)
Znanstveno / umjetničko
područje, polje i grana		BIOMEDICINA I ZDRAVSTVO
Kliničke medicinske znanosti
Dermatovenerologija
Sažetak (engleski)
Background: Paraneoplastic pemphigus (PNP), also called paraneoplastic autoimmune multiorgan syndrome (PAMS), is a rare autoimmune disease with mucocutaneous and multi-organ involvement. PNP/PAMS is typically associated with lymphoproliferative or haematological malignancies, and less frequently with solid malignancies. The mortality rate of PNP/PAMS is elevated owing to the increased risk of severe infections and disease-associated complications, such as bronchiolitis obliterans. Objectives: These guidelines summarize evidence-based and expert-based recommendations (S2k level) for the clinical characterization, diagnosis and management of PNP/PAMS. They have been initiated by the Task Force Autoimmune Blistering Diseases of the European Academy of Dermatology and Venereology with the contribution of physicians from all relevant disciplines. The degree of consent among all task force members was included. Results: Chronic severe mucositis and polymorphic skin lesions are clue clinical characteristics of PNP/PAMS. A complete assessment of the patient with suspected PNP/PAMS, requiring histopathological study and immunopathological investigations, including direct and indirect immunofluorescence, ELISA and, where available, immunoblotting/immunoprecipitation, is recommended to achieve a diagnosis of PNP/PAMS. Detection of anti-envoplakin antibodies and/or circulating antibodies binding to the rat bladder epithelium at indirect immunofluorescence is the most specific tool for the diagnosis of PNP/PAMS in a patient with compatible clinical and anamnestic features. Treatment of PNP/PAMS is highly challenging. Systemic steroids up to 1.5 mg/kg/day are recommended as first-line option. Rituximab is also recommended in patients with PNP/PAMS secondary to lymphoproliferative conditions but might also be considered in cases of PNP/PAMS associated with solid tumours. A multidisciplinary approach involving pneumologists, ophthalmologists and onco-haematologists is recommended for optimal management of the patients. Conclusions: These are the first European guidelines for the diagnosis and management of PNP/PAMS. Diagnostic criteria and therapeutic recommendations will require further validation by prospective studies.
Ključne riječi (engleski)
Jezikengleski
Vrsta publikacijeStručni rad - Stručni rad
Status objaveObjavljen
Vrsta recenzijeRecenziran
Verzija publikacijeObjavljena verzija rada (izdavačev PDF)
Naslov časopisaJournal of the European Academy of Dermatology and Venereology
Brojčani podacivol. 37, br. 6, str. 1118-1134
p-ISSN0926-9959
e-ISSN1468-3083
DOIhttps://doi.org/10.1111/jdv.18931
URN:NBNurn:nbn:hr:105:818244
Datum objave publikacije2023-03-25
URL dokumentahttps://onlinelibrary.wiley.com/doi/10.1111/jdv.18931
Vrsta resursaTekst
Prava pristupaOtvoreni pristup
Uvjeti korištenjaIkona licence Imenovanje-Nekomercijalno 4.0 međunarodna (CC BY-NC 4.0)
Datum i vrijeme pohrane2024-01-09 08:43:32