Rijetki tumor pluća u dječjoj dobi - inflamatorni miofibroblastični tumor

Professional paper - Review paper

• Title (english): A rare tumor of the lung in childhood - inflammatory myofibroblastic tumor
• Author: Mirko Žganjer
• Author: Igor Nikolić
• Author: Ante Čizmić
• Author: Marko Mesić
• Author: Božidar Župančić
• Author's institution: University of Zagreb; School of Medicine
• Scientific / art field, discipline and subdiscipline: BIOMEDICINE AND HEALTHCARE; Clinical Medical Sciences

Abstract (english)

Inflammatory myofibroblastic tumor (IMT) is a rare benign neoplasm, mainly involving the lungs of the children. It represents 0.7% of all lung tumors. It was first described by Brunn in 1939.2 Diagnosis is very difficult and often only possible after resection of the tumor. We would like to present a case of pulmonary IMT in a 13-year-old girl who presented with symptoms like cough, shortness of breath, and chest discomfort. Chest X ray and computed tomography revealed the presence of a right lower lobe lung mass. Its clinical and radiological findings were diverse and non specific. The mass was removed in toto, histopathology confirmed the inflammatory myofibroblastic tumor of the lung. Intraoperative and postoperative courses were uneventful. The patient has been without any signs of relapse 2 years after the surgery.

Abstract (croatian)

Inflamatorni miofibroblastični tumor (IMT) benigna je novotvorina koja uglavnom zahvaća pluća kod djece. Od svih tumora pluća javlja se u 0,7%.1 Brunn je tumor prvi opisao 1939. godine.2 Postavljanje sigurne dijagnoze veoma je teško i često moguće tek nakon resekcije tumora. Mi želimo prikazati 13-godišnju bolesnicu s plućnim IMT-om koja je duže vrijeme kašljala, imala zaduhu i osjećaj nelagode u prsnom košu. Rendgenska snimka, kao i kompjutorizirana tomografija pokazale su prisutnost tumorske mase u donjem plućnom režnju s desne strane. Njezini klinički i radiološki nalazi nisu bili specifični da bi se mogla utvrditi dijagnoza pa se indicirao kirurški zahvat. Sam zahvat i postoperativni tijek protekli su bez komplikacija. Tumor je odstranjen u cijelosti, histološki je potvrđen upalni miofibroblastični tumor pluća. Bolesnica je 2 godine nakon operacije bila bez kliničkih znakova recidiva bolesti.

• Keywords (english): Adolescent; Biopsy, Needle; Female; Humans; Lung Neoplasms / pathology; Lung Neoplasms / surgery; Plasma Cell Granuloma, Pulmonary / pathology; Plasma Cell Granuloma, Pulmonary / surgery; Rare Diseases; Tomography, X-Ray Computed; Treatment Outcome
• Language: croatian
• Publication type: Professional paper - Review paper
• Publication status: Published
• Peer review: Peer review
• Publication version: Published version
• Journal title: Liječnički vjesnik
• Numbering: vol. 136, no. 1-2, pp. 25-27
• p-ISSN: 0024-3477
• URN:NBN: urn:nbn:hr:105:788190
• Publication: 2014-01
• Document URL: http://lijecnicki-vjesnik.hlz.hr/lijecnicki-vjesnik/rijetki-tumor-pluca-u-djecjoj-dobi-inflamatorni-miofibroblasticni-tumor/
• Type of resource: Text
• Access conditions: Open access
• Created on: 2024-03-28 07:59:40